VISKOTT ALDRICH SINDROMI. KASALLIKNING QISQACHA TAVSIFI. KLINIK KUZATUV
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Tadqiqot maqsadi. Viskott-Aldrich sindromi bilan og'rigan bemorning klinik holatini tavsiflash.
Materiallar va metodlar. Ushbu tadqiqotda biz 2007 yilda tug'ilgan o'g'il bolada Viskott-Aldrich sindromi shaklida namoyon bo'lgan birlamchi immunitet tanqisligi klinik ko'rinishini keltiramiz. Bola bolalar gematologiya, onkologiya va klinik immunologiya markazida gematolog va immunolog shifokor nazoratidadir.
Natijalar va muhokamalar. Bolada uning og'ir ahvoli, og'ir intoksikatsiya, gepatosplenomegaliya, tana terisida petechial toshmalar, gemorragik sindrom, qonda kelib chiqishi noma'lum anemiya kabi keng ko'lamli klinik va laboratoriya belgilari mavjud edi. Shuningdek, leykotsitoz, EChT oshishi, trombotsitopeniya holati kuzatildi. Yuqoridagi barcha ko'rsatkichlar va ma'lumotlarni hisobga olgan holda bolaga Birlamchi immunitet tanqisligi, Wiskott-Aldrich sindromi tashxisi qo'yildi .
Xulosa. Ushbu klinik keysga asoslanib, kasalliknig klinik ko'rinishi, shu jumladan ushbu unig belgilari xarakterli triadasi juda o'ziga xos ekanligiga ishonch hosil qilish mumkin. Bu esa shifokorlarga boshqa kasalliklar bilan differentsial tashxis qo'yishda yordam beradi.
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